Unusual presentation of adult Marfan syndrome as a complex diaphragmatic hiatus hernia.
نویسندگان
چکیده
Marfan syndrome is multisystem connective tissue disorder that primarily involves the skeletal, cardiovascular, and ocular systems. The gastrointestinal complications in Marfan syndrome are rare, with only a few case reports described in the literature. We present a 25-year-old woman who presented with acute abdominal pain for 1 day. The imaging features revealed complex diaphragmatic hiatus hernia with organoaxial gastric volvulus. This is a unique case report about an adult patient with Marfan syndrome who presented with symptomatic paraesophageal hernia and organoaxial gastric volvulus.
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عنوان ژورنال:
- Asian journal of surgery
دوره 40 4 شماره
صفحات -
تاریخ انتشار 2017